Identification
BMDB Protein ID BMDBP00067
Secondary Accession Numbers None
Name Ferrochelatase, mitochondrial
Synonyms Not Available
Gene Name FECH
Protein Type Enzyme
Biological Properties
General Function Coenzyme transport and metabolism
Specific Function Catalyzes the ferrous insertion into protoporphyrin IX.
Pathways
  • Porphyrin Metabolism
  • Porphyrin-containing compound metabolism
  • Protoheme biosynthesis
  • Protoheme from protoporphyrin-IX: step 1/1
Reactions
Protoporphyrin IX + Iron → Heme +2 Hydrogen details
GO Classification Not Available
Cellular Location Not Available
Gene Properties
Chromosome Location 24
Locus Not Available
SNPs FECH
Gene Sequence
>1251 bp
ATGGCTGCGGCCTTGCGATCTGCGGGCGTCCTGCTCCGCGATCGGCTGCTGTACGGCGGC
TCAAGGGCCTGTCAGCCACGGAGGTGCCAGTCAGGTGCGGCCACAGCGGCGGCCGCCACG
GAAACCGCCCAGCGTGCCAGAAGCCCCAAGCCTCAGGCTCAGCCGGGGAACAGGAAGCCA
AGGACTGGAATATTGATGCTGAACATGGGGGGCCCGGAAACCGTCGAAGAAGTCCAGGAC
TTCCTTCAGAGGCTCTTTCTGGACCAAGACCTCATGACGCTCCCCGTCCAAGATAAGCTG
GGACCATTCATCGCCAAACGCCGAACCCCCAAAATTCAGGAGCAGTACCGCAGGATTGGA
GGCGGATCGCCCATCAAGATGTGGACCTCCAAGCAGGGGGAAGGCATGGTGAAGCTGCTG
GATGAGCTGTCCCCACACACAGCCCCGCACAAATACTATATTGGATTCCGGTACGTCCAC
CCGTTAACAGAGGAAGCAATTGAAGAGATGGAGAGGGACGGCCTGGAGAGGGCGGTTGCT
TTCACGCAGTACCCCCAGTACAGCTGCTCCACCACAGGCAGCAGCTTAAATGCCATTTAC
AGATACTACAATGAAGTGGGCAGGAAGCCCACCATGAAGTGGAGCACGATCGACAGGTGG
CCCACGCACCCCCTCCTCATCCAGTGCTTTGCTGACCATATTCTGAAAGAGCTGGATCAC
TTTCCTCCTGAGAAGAGACGCGAGGTGGTCATTCTTTTTTCTGCTCACTCACTGCCAATG
TCTGTGGTCAACAGAGGGGACCCCTATCCTCAAGAGGTAGGCGCCACTGTCCAGAGAGTC
ATGGACAAGCTGGGTTACTCCAACCCCTACCGACTTGTTTGGCAGTCCAAGGTTGGCCCG
ATGCCCTGGCTGGGTCCTCAGACAGACGAGGCCATCAAAGGGCTTTGTAAGAGGGGAAGG
AAGAACATCCTTTTAGTGCCAATAGCGTTTACCAGCGATCACATCGAAACGCTCTATGAG
CTGGACATCGAGTACTCTCAAGTTCTAGCCAGTGAGTGTGGACTTGAAAACATCAGAAGA
GCGGAGTCTCTTAATGGAAACCCACTGTTCTCGAAGGCCCTGGCCGACCTGGTGCACTCA
CACCTCCAGTCCAAGGAGCGCTGCTCCACACAGCTGACTCTGAGCTGTCCGCTCTGCGTG
AACCCTACCTGCAGGGAGACCAAATCCTTCTTCACCAGCCAGCAGCTGTGA
Protein Properties
Number of Residues 416
Molecular Weight 46935.0
Theoretical pI 9.04
Pfam Domain Function Not Available
Signals
  • None
Transmembrane Regions Not Available
Protein Sequence
>Ferrochelatase, mitochondrial
MAAALRSAGVLLRDRLLYGGSRACQPRRCQSGAATAAAATETAQRARSPKPQAQPGNRKP
RTGILMLNMGGPETVEEVQDFLQRLFLDQDLMTLPVQDKLGPFIAKRRTPKIQEQYRRIG
GGSPIKMWTSKQGEGMVKLLDELSPHTAPHKYYIGFRYVHPLTEEAIEEMERDGLERAVA
FTQYPQYSCSTTGSSLNAIYRYYNEVGRKPTMKWSTIDRWPTHPLLIQCFADHILKELDH
FPPEKRREVVILFSAHSLPMSVVNRGDPYPQEVGATVQRVMDKLGYSNPYRLVWQSKVGP
MPWLGPQTDEAIKGLCKRGRKNILLVPIAFTSDHIETLYELDIEYSQVLASECGLENIRR
AESLNGNPLFSKALADLVHSHLQSKERCSTQLTLSCPLCVNPTCRETKSFFTSQQL
GenBank ID Protein AAA79169.1
UniProtKB/Swiss-Prot ID P22600
UniProtKB/Swiss-Prot Entry Name HEMH_BOVIN
PDB IDs
GenBank Gene ID L34173
GeneCard ID FECH
GenAtlas ID Not Available
HGNC ID Not Available
References
General References Not Available