Identification
BMDB Protein ID BMDBP00093
Secondary Accession Numbers
  • BMDBP03150
Name Dihydroorotate dehydrogenase (quinone), mitochondrial
Synonyms Not Available
Gene Name DHODH
Protein Type Enzyme
Biological Properties
General Function Nucleotide transport and metabolism
Specific Function Catalyzes the conversion of dihydroorotate to orotate with quinone as electron acceptor.
Pathways
  • Orotate from (S)-dihydroorotate (quinone route): step 1/1
  • Pyrimidine Metabolism
  • UMP biosynthesis via de novo pathway
Reactions
L-Dihydroorotic acid + Quinone → Orotic acid + quinol details
GO Classification Not Available
Cellular Location Not Available
Gene Properties
Chromosome Location 18
Locus Not Available
SNPs DHODH
Gene Sequence
>1188 bp
ATGGCGTGGAGGCAGCTCAAAAAGCGGGCCCAGGATGCCATGGTGATCCTGGGGGGCGGA
GGACTTCTCTTTGCCTCCTACTTGACGGCCACGGGGGATGAGCACTTCTACGCTGAACTC
TTGATGCCGTCTCTGCAGCGGCTGCTGGACCCTGAGACAGCCCACAGGCTGGCTGTTCGC
TTCACCTCCCTGGGGCTCCTTCCTCGAACCACGTTTCAAGACTCTGACATGCTGGAAGTG
AGAGTCCTTGGCCATAAATTCCGAAATCCAGTGGGAATCGCCGCAGGATTTGACAAGCAC
GGGGAAGCGGTGGATGGCCTTTACAAGATGGGCTTTGGTTTTGTTGAGATAGGCAGTGTA
ACCCCAGAACCTCAGGAAGGAAACCCCAGGCCCAGGGTCTTCCGCCTCCCAGAAGACCAA
GCTATCATTAACAGATACGGATTTAACAGTCATGGACTCTCAGTGGTGGAACACAGGTTA
CGGGCCAGACAGCAGACACAGGCCAGACTCACAGAAGATGGGCTGCCGCTGGGAATAAAC
CTGGGGAAGAATAAGACCTCGGTGGACGCTGCCTCCGACTATGCAGAGGGGGTTCGAGTC
CTGGGTCCCTTGGCTGACTACCTGGTAGTGAATGTGTCCAGTCCCAACACGGCTGGGCTG
CGGAGCCTTCAGGGAAAGGCCGAACTGCGCCGCCTGCTGACCAAGGTGCTGCAGGAGAGG
GATGCCCTGAAGGTGGCCCACAAGCCAGCTGTCCTGGTGAAGATTGCTCCCGACCTCACA
GCCCAGGACAAGGAGGATATTGCCAGCGTGGTGAGAGAGTTGGGCATCGATGGACTGATC
GTCACAAACAGCACAGTGAGTCGCCCTGCCAGCCTCCAGGGTGCCCTGCGCTCTGAACCA
GGAGGGCTGAGCGGGAAGCCCCTCAGGGATTTATCAACGCAAACCATCCGGGAGATGTAT
GCACTCACCCAAGGCAGAGTTCCCATCGTCGGGGTTGGCGGTGTCAGCAGCGGGCAGGAT
GCGCTGGAGAAGATCCGCGCGGGAGCCTCCCTCGTGCAGCTGTACACGGCCCTCACCTAC
CGGGGCCCGCCCGTAGTGGGCGGGGTCAAGCGGGAGCTGGAAGCCCTTTTGAAGGAGCAG
GGTTTTGCCAGAGTCACAGACGCCATTGGGGCAGATCATCGGAGGTGA
Protein Properties
Number of Residues 395
Molecular Weight 42776.0
Theoretical pI 9.96
Pfam Domain Function Not Available
Signals
  • None
Transmembrane Regions
  • 11-30
Protein Sequence
>Dihydroorotate dehydrogenase, mitochondrial
MAWRQLKKRAQDAMVILGGGGLLFASYLTATGDEHFYAELLMPSLQRLLDPETAHRLAVR
FTSLGLLPRTTFQDSDMLEVRVLGHKFRNPVGIAAGFDKHGEAVDGLYKMGFGFVEIGSV
TPEPQEGNPRPRVFRLPEDQAIINRYGFNSHGLSVVEHRLRARQQTQARLTEDGLPLGIN
LGKNKTSVDAASDYAEGVRVLGPLADYLVVNVSSPNTAGLRSLQGKAELRRLLTKVLQER
DALKVAHKPAVLVKIAPDLTAQDKEDIASVVRELGIDGLIVTNSTVSRPASLQGALRSEP
GGLSGKPLRDLSTQTIREMYALTQGRVPIVGVGGVSSGQDALEKIRAGASLVQLYTALTY
RGPPVVGGVKRELEALLKEQGFARVTDAIGADHRR
GenBank ID Protein AAX08824.1
UniProtKB/Swiss-Prot ID Q5E9W3
UniProtKB/Swiss-Prot Entry Name PYRD_BOVIN
PDB IDs
GenBank Gene ID BT020807
GeneCard ID DHODH
GenAtlas ID Not Available
HGNC ID Not Available
References
General References Not Available