Identification
BMDB Protein ID BMDBP00687
Secondary Accession Numbers
  • BMDBP03026
Name Aconitate hydratase, mitochondrial
Synonyms Not Available
Gene Name ACO2
Protein Type Enzyme
Biological Properties
General Function Energy production and conversion
Specific Function Catalyzes the isomerization of citrate to isocitrate via cis-aconitate.
Pathways
  • Carbohydrate metabolism
  • Isocitrate from oxaloacetate: step 2/2
  • Tricarboxylic acid cycle
Reactions
Citric acid → cis-Aconitic acid + Water details
cis-Aconitic acid + Water → Isocitric acid details
Citric acid → Isocitric acid details
GO Classification Not Available
Cellular Location Not Available
Gene Properties
Chromosome Location 5
Locus 5q35
SNPs ACO2
Gene Sequence
>2343 bp
ATGGCGCCTTACAGCCTACTGGTGTCCCGGCTGCAGAAAGCCCTGGGTGCGCGGCAGTAC
CATGTGGCCTCAGTCCTGTGCCAACGGGCCAAGGTGGCCATGAGCCACTTTGAACCCAAT
GAGTACATCCGCTATGACCTGCTCGAGAAGAACATTAACATTGTCCGCAAACGGCTGAAC
CGGCCTCTGACCCTCTCAGAGAAGATCGTGTATGGACACCTGGATGACCCGGCCAACCAG
GAGATCGAGCGGGGCAAGACATACCTGCGGCTGCGGCCTGACCGCGTGGCCATGCGGGAT
GCCACGGCCCAGATGGCCATGCTGCAGTTCATCAGCAGCGGCCTGCCCAAGGTGGCCGTG
CCGTCCACCATCCACTGTGACCATTTGATCGAGGCCCAGCTCGGCGGGGAGAAGGACCTG
CGTCGGGCCAAGGACATAAACCAGGAAGTGTATAATTTCCTGGCCACTGCAGGTGCCAAG
TACGGCGTGGGCTTCTGGAGGCCTGGCTCTGGAATCATTCACCAGATCATTCTGGAAAAC
TATGCGTACCCTGGGGTTCTTCTGATTGGCACTGATTCCCACACCCCTAATGGCGGTGGC
CTGGGAGGCATCTGCATTGGAGTCGGGGGTGCTGATGCCGTGGACGTCACGGCTGGGATC
CCCTGGGAGTTGAAGTGCCCCAAGGTGATTGGCGTGAAGCTGACAGGCTCCCTCTCTGGC
TGGACCTCACCTAAAGATGTGATCCTGAAGGTGGCGGGTATCCTCACAGTGAAAGGTGGC
ACGGGCGCCATCGTGGAGTACCACGGGCCTGGAGTAGACTCCATCTCCTGCACCGGCATG
GCGACCATCTGCAACATGGGTGCAGAAATCGGGGCCACCACTTCGGTGTTCCCTTACAAC
CACAGGATGAAGAAATACCTGAGCAAGACAGGCCGGGCAGATATTGCCAACCTTGCTGAT
GAATTCAAGGATCACTTGGTACCTGACTCTGGCTGCCATTATGACCAACTGATTGAAATT
AACCTCAGTGAGCTGAAGCCGCACATCAATGGGCCCTTTACCCCTGACCTGGCTCACCCT
GTGGCAGAAGTGGGCAGTGTGGCAGAGAAGGAGGGGTGGCCCTTGGACATCCGAGTTGGT
CTGATTGGCAGCTGTACCAACTCCAGCTATGAAGACATGGGCCGCTCCGCAGCCGTGGCC
AAGCAGGCGCTGGCCCACGGACTCCAGTGCAAATCCCAGTTCACCATCACCCCAGGCTCG
GAGCAGATCCGCGCCACCATCGAGCGGGATGGCTATGCACAGATCCTGAGGGATGTGGGT
GGCATCGTCCTGGCCAATGCCTGCGGGCCCTGCATTGGCCAATGGGACAGGAAGGACATC
AAGAAGGGGGAGAAGAACACCATCGTCACCTCCTACAACAGGAACTTCACAGGCCGCAAC
GACGCAAATCCTGAGACCCACGCCTTCGTCACGTCCCCAGAGATTGTCACAGCCCTGGCC
ATTGCTGGCACCCTCAAGTTCAACCCAGAGACTGACTTCCTGACGGGCAAGGACGGCAAG
AAGTTCAAGCTGGAGGCTCCAGACGCAGATGAGCTTCCTCGAGCGGAGTTCGACCCCGGA
CAGGACACCTACCAGCACCCCCCCAAGGACAGCAGTGGGCAGCAGGTGGACGTGAGTCCC
ACCAGCCAGCGCCTGCAGCTCCTGGAGCCTTTCGACAAGTGGGACGGCCGAGACCTGGAG
GACCTGCAGATCCTCATCAAGGTCAAAGGGAAGTGTACCACCGACCACATCTCGGCTGCT
GGTCCCTGGCTCAAGTTCCGTGGGCACCTGGACAACATCTCCAACAACCTGCTCATTGGC
GCCATCAACGTGGAAAACGGCAAGGCCAACTCCGTGCGCAATGCCGTCACCCAGGAGTTC
GGTCCTGTCCCTGACACCGCCCGCTACTACAAGAAACACGGCATCCGGTGGGTGGTGATT
GGAGATGAAAACTATGGTGAGGGCTCGAGCCGGGAGCACGCAGCCCTGGAGCCTCGCCAC
CTCGGGGGCCGGGCCATCATCACCAAGAGCTTTGCCAGGATCCACGAAACCAACCTGAAG
AAGCAGGGCCTGCTGCCCCTCACCTTCGCTGACCCAGCTGACTACAACAAGATTCACCCT
GTGGACAAGCTGACCATCAAGGGCCTGAAGGACTTTGCCCCCGGCAAGCCGCTGACATGT
ATCATCAAGCACCCCAACGGGACCCAGGAGACCATCCTCCTGAACCACACCTTCAACGAG
ACCCAGATCGAGTGGTTCCGCGCCGGCAGCGCGCTCAACAGGATGAAGGAGCTGCAGAAG
TGA
Protein Properties
Number of Residues 780
Molecular Weight 85359.0
Theoretical pI 7.9
Pfam Domain Function Not Available
Signals
  • None
Transmembrane Regions Not Available
Protein Sequence
>Aconitate hydratase, mitochondrial
MAPYSLLVSRLQKALGARQYHVASVLCQRAKVAMSHFEPNEYIRYDLLEKNINIVRKRLN
RPLTLSEKIVYGHLDDPANQEIERGKTYLRLRPDRVAMQDATAQMAMLQFISSGLPKVAV
PSTIHCDHLIEAQLGGEKDLRRAKDINQEVYNFLATAGAKYGVGFWRPGSGIIHQIILEN
YAYPGVLLIGTDSHTPNGGGLGGICIGVGGADAVDVMAGIPWELKCPKVIGVKLTGSLSG
WTSPKDVILKVAGILTVKGGTGAIVEYHGPGVDSISCTGMATICNMGAEIGATTSVFPYN
HRMKKYLSKTGRADIANLADEFKDHLVPDSGCHYDQLIEINLSELKPHINGPFTPDLAHP
VAEVGSVAEKEGWPLDIRVGLIGSCTNSSYEDMGRSAAVAKQALAHGLQCKSQFTITPGS
EQIRATIERDGYAQILRDVGGIVLANACGPCIGQWDRKDIKKGEKNTIVTSYNRNFTGRN
DANPETHAFVTSPEIVTALAIAGTLKFNPETDFLTGKDGKKFKLEAPDADELPRAEFDPG
QDTYQHPPKDSSGQQVDVSPTSQRLQLLEPFDKWDGRDLEDLQILIKVKGKCTTDHISAA
GPWLKFRGHLDNISNNLLIGAINVENGKANSVRNAVTQEFGPVPDTARYYKKHGIRWVVI
GDENYGEGSSREHAALEPRHLGGRAIITKSFARIHETNLKKQGLLPLTFADPADYNKIHP
VDKLTIKGLKDFAPGKPLTCIIKHPNGTQETILLNHTFNETQIEWFRAGSALNRMKELQK
GenBank ID Protein CAA90177.1
UniProtKB/Swiss-Prot ID P20004
UniProtKB/Swiss-Prot Entry Name ACON_BOVIN
PDB IDs
GenBank Gene ID Z49931
GeneCard ID ACO2
GenAtlas ID Not Available
HGNC ID Not Available
References
General References Not Available