Identification
BMDB Protein ID BMDBP00871
Secondary Accession Numbers
  • BMDBP03038
Name Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
Synonyms Not Available
Gene Name ACADM
Protein Type Enzyme
Biological Properties
General Function Lipid transport and metabolism
Specific Function Acyl-CoA dehydrogenase specific for acyl chain lengths of 4 to 16 that catalyzes the initial step of fatty acid beta-oxidation. Utilizes the electron transfer flavoprotein (ETF) as an electron acceptor to transfer electrons to the main mitochondrial respiratory chain via ETF-ubiquinone oxidoreductase (ETF dehydrogenase).
Pathways
  • Lipid metabolism
  • Mitochondrial fatty acid beta-oxidation
Reactions
Acrylyl-CoA + electron-transfer flavoprotein → Propionyl-CoA + Reduced electron-transfer flavoprotein details
GO Classification Not Available
Cellular Location Not Available
Gene Properties
Chromosome Location 3
Locus Not Available
SNPs ACADM
Gene Sequence
>1266 bp
ATGATCGCGCTGTTTAGGCGAAGCTGCGGGGTACTGAGAAGTCTTTCTCATTTTGACTGG
AGATCACAACATACAAAAACTGCCCTACAACGTGAGCCAGGATCAGGATTTAGTTTTGAA
TTCACTGAACAACAGAAAGAATTTCAAGCTACTGCTCGTAAATTTGCCAGGGAGGAAATA
ATTCCACTTGCTGCAGAATATGATAAAACCGGCGAGTACCCTGTCCCATTAATTAAAAGA
GCCTGGGAGCTTGGTTTAATGAATACACACATTCCAGAAAGTTGTGGAGGTCTTGGACTT
GGAACTTTTGATAGCTGTTTAATTTCTGAAGAATTGGCTTATGGATGTACAGGGGTTCAG
ACTGCTATTGAAGCAAATTCTCTAGGGCAAATGCCTGTTATTATTGCTGGAAATGATCAA
CAACAAAAGAAATATTTGGGGAGAATGACTGAGGAGCCATTAATGTGTGCCTATTGTGTA
ACAGAACCTGTAGCAGGCTCTGATGTAGCTGGTATAAAAACCAAAGCAGAAAAGAAAGGA
GATGAGTATATTATTAATGGTCAGAAGATGTGGATCACCAATGGAGGAAAAGCTAATTGG
TATTTTTTATTGGCTCGTTCTGATCCGGATCCTAAGGCTCCTGCTAGTAAAGCCTTTACT
GGCTTTATTGTGGAAGCAGACACCCCAGGAGTACAGATTGGAAGAAAGGAATTAAATATG
GGACAGCGATGTTCAGATACAAGAGGAATTGTCTTTGAAGATGTGAGAGTGCCCAAGGAA
AATGTTTTAATTGGTGAGGGAGCTGGTTTCAAAATTGCAATGGGAGCATTTGATAAAACC
AGACCACCAGTAGCAGCTGCTGCTGTGGGACTAGCACAGAGAGCTTTGGATGAAGCTACC
AAGTATGCCCTGGAGAGAAAAACTTTTGGAAAGCTGCTTATAGAGCACCAAGGAATATCA
TTTTTGCTGGCTGAAATGGCAATGAAAGTTGAACTAGCTAGATTGAGTTACCAGAGAGCA
GCTTGGGAAGTTGATTCTGGTCGCCGAAATACCTATTATGCCTCTATTGCAAAGGCATAT
GCTGGAGATATCGCAAATCAGTTAGCTTCTGATGCTGTTCAGATTTTTGGAGGCAATGGA
TTTAATACTGAATATCCTGTAGAAAAATTAATGAGAGATGCCAAGATCTATCAGATTTAT
GAAGGTACAGCACAAATTCAAAGGCTTATTATAGCCCGTGAACACATTGGCAGGTATAAG
AAGTAA
Protein Properties
Number of Residues 421
Molecular Weight 46573.0
Theoretical pI 8.24
Pfam Domain Function Not Available
Signals
  • None
Transmembrane Regions Not Available
Protein Sequence
>Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
MIALFRRSCGVLRSLSHFDWRSQHTKTALQREPGSGFSFEFTEQQKEFQATARKFAREEI
IPLAAEYDKTGEYPVPLIKRAWELGLMNTHIPESCGGLGLGTFDSCLISEELAYGCTGVQ
TAIEANSLGQMPVIIAGNDQQQKKYLGRMTEEPLMCAYCVTEPVAGSDVAGIKTKAEKKG
DEYIINGQKMWITNGGKANWYFLLARSDPDPKAPASKAFTGFIVEADTPGVQIGRKELNM
GQRCSDTRGIVFEDVRVPKENVLIGEGAGFKIAMGAFDKTRPPVAAAAVGLAQRALDEAT
KYALERKTFGKLLIEHQGISFLLAEMAMKVELARLSYQRAAWEVDSGRRNTYYASIAKAY
AGDIANQLASDAVQIFGGNGFNTEYPVEKLMRDAKIYQIYEGTAQIQRLIIAREHIGRYK
K
GenBank ID Protein ABS70460.1
UniProtKB/Swiss-Prot ID Q3SZB4
UniProtKB/Swiss-Prot Entry Name ACADM_BOVIN
PDB IDs
GenBank Gene ID EU009460
GeneCard ID ACADM
GenAtlas ID Not Available
HGNC ID Not Available
References
General References Not Available