Showing Protein Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial (BMDBP00888)
Identification | |||||
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BMDB Protein ID | BMDBP00888 | ||||
Secondary Accession Numbers | None | ||||
Name | Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial | ||||
Synonyms | Not Available | ||||
Gene Name | ACADSB | ||||
Protein Type | Enzyme | ||||
Biological Properties | |||||
General Function | Lipid transport and metabolism | ||||
Specific Function | Has greatest activity toward short branched chain acyl-CoA derivative such as (s)-2-methylbutyryl-CoA, isobutyryl-CoA, and 2-methylhexanoyl-CoA as well as toward short straight chain acyl-CoAs such as butyryl-CoA and hexanoyl-CoA. Can use valproyl-CoA as substrate and may play a role in controlling the metabolic flux of valproic acid in the development of toxicity of this agent (By similarity). | ||||
Pathways |
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Reactions |
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GO Classification | Not Available | ||||
Cellular Location | Not Available | ||||
Gene Properties | |||||
Chromosome Location | 26 | ||||
Locus | Not Available | ||||
SNPs | ACADSB | ||||
Gene Sequence |
>1299 bp ATGGAGCGAGCTACTGTTCGGCTGCTGCGCGGCGGCGCGCTGCTACGAAGAAACTTCCCA AGCTGCCTGTCTTCCTGGAAAACTCCTCCTCATGCCCTAAATTCTTCTCAGTCAGAAGCT CAGCTCAAAGCGACAAGCAATGGACCACCTCTTGCCCCTCTGCAAACATTTACGGATGAG GAGATGATGATAAAGAGCGCAGTTAAAAAATTTGCCCAGGAACAAGTTGCTCCTTTTGTT TCAAAAATGGATGAAGATTCAAAAATGGAAAAATCCGTAATACAAGGATTATTTCAACAA GGGTTGATGGGTATTGAAATTGACACAAAATATGGAGGAACAGGAGCTTCATTTTTTTCC TCTGTCCTAGTGATAGAGGAGTTAGCCAAAGTTGATGCATCTGTGGCTCTGGTATGTGAC ATTCAGAACACATTAATTAACAGGATGATTGGAAAATATGGAACAGAAGAACAGAAGGCT ACCTATTTGCCCAAGCTAGCTACAGAAAAGGCATCAAGTATCTGCATTTCAGAGACTGGA GCAGGTAGCGATTCATTTGCTATGAAGACCAGAGCTGATAAAAAGGGAGATTATTACATC ATCAATGGGTCAAAGATGTGGATTAGCAGTGCTGAGATTGCTGGGCTGTTCGTGGTGATG GCAAATGCAGACTTTTCTGCTGGGTATAAAGGAATTACCTGCTTCTTGGTCGATGGTGAT ACCGAGGGCCTTCATGTAGGGAAACCAGAGAACAAATTGGGAATCAGAGCATCTTCCACC TGCCCAGTCACATTTGAAAATGTCAAGGTTCCAAAAACAAATATCCTGGGGCAAGTTGGG CACGGCTATAAGTATGCCATCGGGAGTCTTAATGAAGGCAGAATAGGAATCGCTGCACAG ATGCTGGGAGTGGCTCAAGGCTGTTTTGACTACACTATTCCATATATTAAAGAAAGGAAA CAATTTGGCCGAAGGGTATTTGATTTTCAGGGGCTCCAACACCAAGTGGCTCACATGGCC ACCCAGCTGGAAGCTGCTCGACTCCTGACATACAATGCTGCGAGGCTCTTAGAGGCTGGG AGGCCGATGATTAAAGAAGCATCTATGGCCAAATACCATGCGTCAGAGCTGGCAGGCCTC ATTACCAGCAAGTGTATCGAGTGGATGGGAGGAGTGGGCTACACCAAAAGTTACCCTGTG GAAAAATATTTCCGAGATGCGAAGATTGGCACAATTTATGAAGGAACTTCAAATATCCAG CTGAACACCATCGCAAAGTGCATCAGTGCGGAATACTGA |
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Protein Properties | |||||
Number of Residues | 432 | ||||
Molecular Weight | 47123.0 | ||||
Theoretical pI | 8.65 | ||||
Pfam Domain Function | Not Available | ||||
Signals |
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Transmembrane Regions | Not Available | ||||
Protein Sequence |
>Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial MERATVRLLRGGALLRRNFPSCLSSWKTPPHALNSSQSEAQLKATSNGPPLAPLQTFTDE EMMIKSAVKKFAQEQVAPFVSKMDEDSKMEKSVIQGLFQQGLMGIEIDTKYGGTGASFFS SVLVIEELAKVDASVALVCDIQNTLINRMIGKYGTEEQKATYLPKLATEKASSICISETG AGSDSFAMKTRADKKGDYYIINGSKMWISSAEIAGLFVVMANADFSAGYKGITCFLVDGD TEGLHVGKPENKLGIRASSTCPVTFENVKVPKTNILGQVGHGYKYAIGSLNEGRIGIAAQ MLGVAQGCFDYTIPYIKERKQFGRRVFDFQGLQHQVAHMATQLEAARLLTYNAARLLEAG RPMIKEASMAKYHASELAGLITSKCIEWMGGVGYTKSYPVEKYFRDAKIGTIYEGTSNIQ LNTIAKCISAEY |
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External Links | |||||
GenBank ID Protein | AAI22699.1 | ||||
UniProtKB/Swiss-Prot ID | Q5EAD4 | ||||
UniProtKB/Swiss-Prot Entry Name | ACDSB_BOVIN | ||||
PDB IDs | Not Available | ||||
GenBank Gene ID | BC122698 | ||||
GeneCard ID | ACADSB | ||||
GenAtlas ID | Not Available | ||||
HGNC ID | Not Available | ||||
References | |||||
General References | Not Available |