Identification
BMDB Protein ID BMDBP00953
Secondary Accession Numbers None
Name Ornithine carbamoyltransferase, mitochondrial
Synonyms Not Available
Gene Name OTC
Protein Type Enzyme
Biological Properties
General Function Amino acid transport and metabolism
Specific Function Not Available
Pathways
  • Arginine and Proline Metabolism
  • L-citrulline from L-ornithine and carbamoyl phosphate: step 1/1
  • Nitrogen metabolism
  • Urea Cycle
Reactions
Carbamoylphosphate + Ornithine → Hydrogen phosphate + Citrulline details
GO Classification Not Available
Cellular Location Not Available
Gene Properties
Chromosome Location X
Locus Not Available
SNPs OTC
Gene Sequence
>1065 bp
ATGCTGTTTCATCTAAGGACCCTGTTGAACAATGCAGCTCTTAGAAATGGTCACAATTTC
GTGGTTCGAAATTTTCGATGTGGGCAACCACTACAGGATAAAGTACAGCTGAAGGGCCGT
GACCTCCTCACTCTAAAGAACTTTACAGGAGAAGAAATTAAGTATATGCTATGGCTATCA
GCAGATCTGAAATTCAGGATAAAACAGAAAGGAGAGTATTTGCCTTTACTGCAAGGGAAG
TCCTTAGGCATGATTTTTGAAAAAAGAAGTACTCGAACAAGATTGTCCACAGAAACAGGC
TTTGCACTTCTGGGAGGACACCCTTGTTTTCTTACTACGGACGATATTCATTTGGGTGTG
AATGAAAGTCTCACAGATACAGCCCGTGTGTTGTCTAGCATGACAGATGCCGTGCTGGCG
CGAGTGTACAAACAATCAGATCTGGACCTCCTGGCTAAAGAAGCTTCCATCCCAATTGTC
AATGGGCTGTCGGATTTGTACCACCCTATCCAGATCCTGGCTGATTACCTCACGCTCCAG
GAACACTACGGCTCTCTGAAAGGCCTTACCCTCAGCTGGATTGGGGATGGGAATAACATC
CTGCACTCCATCATGATGAGTGCGGCTAAATTCGGGATGCACCTTCAGGTGGCTACCCCA
AAGGGTTATGAGCCGGATCCCAGTATAACCAAGATGGCAGAGCAGTATGCCAAGGAGAAC
GGTACCAAGCTGTCGCTGACAAATGATCCATTGGAAGCAGCTTGTGGAGGCAATGTATTA
ATTACAGACACTTGGATAAGCATGGGACAAGAAGAGGAGAAGAAAAAGCGGCTCCAGGCT
TTCCAAGGTTACCAGGTTACAATGAAGACTGCTAAAGTTGCTGCCCCTGACTGGACATTT
TTACACTGCTTGCCCAGAAAGCCAGAAGAAGTGGACGATGAAGTGTTTTATTCTCCACGA
TCTCTTGTATCCCCAGAGGCCGAAAACAGAAAGTGGACAATCATGGCTGTCATGGTATCC
CTGCTGACAGATTATTCGCCTCAGCTCCAGAAGCCAAAGTTTTGA
Protein Properties
Number of Residues 354
Molecular Weight 39842.0
Theoretical pI 8.3
Pfam Domain Function Not Available
Signals
  • None
Transmembrane Regions
  • 40-60
  • 151-173
  • 178-200
  • 266-286
  • 306-326
  • 331-351
  • 420-440
Protein Sequence
>Ornithine carbamoyltransferase, mitochondrial
MLFHLRTLLNNAALRNGHNFVVRNFRCGQPLQDKVQLKGRDLLTLKNFTGEEIKYMLWLS
ADLKFRIKQKGEYLPLLQGKSLGMIFEKRSTRTRLSTETGFALLGGHPCFLTTDDIHLGV
NESLTDTARVLSSMTDAVLARVYKQSDLDLLAKEASIPIVNGLSDLYHPIQILADYLTLQ
EHYGSLKGLTLSWIGDGNNILHSIMMSAAKFGMHLQVATPKGYEPDPSITKMAEQYAKEN
GTKLSLTNDPLEAACGGNVLITDTWISMGQEEEKKKRLQAFQGYQVTMKTAKVAAPDWTF
LHCLPRKPEEVDDEVFYSPRSLVSPEAENRKWTIMAVMVSLLTDYSPQLQKPKF
GenBank ID Protein AAF61405.1
UniProtKB/Swiss-Prot ID Q9N1U7
UniProtKB/Swiss-Prot Entry Name OTC_BOVIN
PDB IDs
GenBank Gene ID AF134841
GeneCard ID OTC
GenAtlas ID Not Available
HGNC ID Not Available
References
General References Not Available