Showing Protein 5-demethoxyubiquinone hydroxylase, mitochondrial (BMDBP01936)
Identification | |
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BMDB Protein ID | BMDBP01936 |
Secondary Accession Numbers | None |
Name | 5-demethoxyubiquinone hydroxylase, mitochondrial |
Synonyms | Not Available |
Gene Name | COQ7 |
Protein Type | Enzyme |
Biological Properties | |
General Function | Coenzyme transport and metabolism |
Specific Function | Catalyzes the hydroxylation of 2-polyprenyl-3-methyl-6-methoxy-1,4-benzoquinol (DMQH2) during ubiquinone biosynthesis. Has also a structural role in the COQ enzyme complex, stabilizing other COQ polypeptides. Involved in lifespan determination in a ubiquinone-independent manner. |
Pathways |
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Reactions | Not Available |
GO Classification | Not Available |
Cellular Location | Not Available |
Gene Properties | |
Chromosome Location | 25 |
Locus | Not Available |
SNPs | COQ7 |
Gene Sequence |
>654 bp ATGAGTTGTGCCCGGGCGTTGGCGGCTTGCTGCCTGTGGCGGCTGCGCACAGGCGCCCTG CAGCCCCTCTCAGCCTATGGAAGAAGAATCAGTGTCAGATTTTGCAGTTCGGGAATGACC TTAGACAATATCAATAGGGAAGCTGTGGATCGAATAATCCGGGTGGATCATGCAGGTGAA TATGGAGCGAACCGCATCTATGCAGGGCAGATGGCCGTCCTGGGTCGGACAAGCATCGGG CCGGTCATTCAGAAAATGTGGGACCAAGAAAAGGACCACTTGAAAAAGTTCAATGAGCTG ATGGTTGCATTCAGGGTGCGGCCTACCGTCCTCATGCCCTTTTGGAACGTGGTGGGGTTT GCACTGGGCGCCGGAACTGCCCTGCTTGGGAAGGAGGGCGCCATGGCCTGCACAGTGGCC GTGGAAGAGTCCATCGCACACCACTACAACAACCAGATCAGGACGCTGATGGAGAAGGAG CCTGAAAAATACGAGGAGCTTCTGCAGGTGATCAAGAAATTTCGGGATGAAGAGCTTGAG CACCATGACATAGGCCTCGAACATGACGCAGAACTGGCTCCAGCATATGTCGTTCTGAAG AGCGTTATCCAGGCAGGATGCAAAGTGGCGATATATTTATCAGAAAGACTTTAA |
Protein Properties | |
Number of Residues | 217 |
Molecular Weight | 24361.0 |
Theoretical pI | 7.85 |
Pfam Domain Function | Not Available |
Signals |
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Transmembrane Regions | Not Available |
Protein Sequence |
>Ubiquinone biosynthesis protein COQ7 homolog MSCARALAACCLWRLRTGALQPLSAYGRRISVRFCSSGMTLDNINREAVDRIIRVDHAGE YGANRIYAGQMAVLGRTSIGPVIQKMWDQEKDHLKKFNELMVAFRVRPTVLMPFWNVVGF ALGAGTALLGKEGAMACTVAVEESIAHHYNNQIRTLMEKEPEKYEELLQVIKKFRDEELE HHDIGLEHDAELAPAYVVLKSVIQAGCKVAIYLSERL |
External Links | |
GenBank ID Protein | AAI09579.1 |
UniProtKB/Swiss-Prot ID | Q2TBW2 |
UniProtKB/Swiss-Prot Entry Name | COQ7_BOVIN |
PDB IDs | Not Available |
GenBank Gene ID | BC109578 |
GeneCard ID | COQ7 |
GenAtlas ID | Not Available |
HGNC ID | Not Available |
References | |
General References | Not Available |