Identification
BMDB Protein ID BMDBP01936
Secondary Accession Numbers None
Name 5-demethoxyubiquinone hydroxylase, mitochondrial
Synonyms Not Available
Gene Name COQ7
Protein Type Enzyme
Biological Properties
General Function Coenzyme transport and metabolism
Specific Function Catalyzes the hydroxylation of 2-polyprenyl-3-methyl-6-methoxy-1,4-benzoquinol (DMQH2) during ubiquinone biosynthesis. Has also a structural role in the COQ enzyme complex, stabilizing other COQ polypeptides. Involved in lifespan determination in a ubiquinone-independent manner.
Pathways
  • Cofactor biosynthesis
  • Ubiquinone Biosynthesis
Reactions Not Available
GO Classification Not Available
Cellular Location Not Available
Gene Properties
Chromosome Location 25
Locus Not Available
SNPs COQ7
Gene Sequence
>654 bp
ATGAGTTGTGCCCGGGCGTTGGCGGCTTGCTGCCTGTGGCGGCTGCGCACAGGCGCCCTG
CAGCCCCTCTCAGCCTATGGAAGAAGAATCAGTGTCAGATTTTGCAGTTCGGGAATGACC
TTAGACAATATCAATAGGGAAGCTGTGGATCGAATAATCCGGGTGGATCATGCAGGTGAA
TATGGAGCGAACCGCATCTATGCAGGGCAGATGGCCGTCCTGGGTCGGACAAGCATCGGG
CCGGTCATTCAGAAAATGTGGGACCAAGAAAAGGACCACTTGAAAAAGTTCAATGAGCTG
ATGGTTGCATTCAGGGTGCGGCCTACCGTCCTCATGCCCTTTTGGAACGTGGTGGGGTTT
GCACTGGGCGCCGGAACTGCCCTGCTTGGGAAGGAGGGCGCCATGGCCTGCACAGTGGCC
GTGGAAGAGTCCATCGCACACCACTACAACAACCAGATCAGGACGCTGATGGAGAAGGAG
CCTGAAAAATACGAGGAGCTTCTGCAGGTGATCAAGAAATTTCGGGATGAAGAGCTTGAG
CACCATGACATAGGCCTCGAACATGACGCAGAACTGGCTCCAGCATATGTCGTTCTGAAG
AGCGTTATCCAGGCAGGATGCAAAGTGGCGATATATTTATCAGAAAGACTTTAA
Protein Properties
Number of Residues 217
Molecular Weight 24361.0
Theoretical pI 7.85
Pfam Domain Function Not Available
Signals
  • None
Transmembrane Regions Not Available
Protein Sequence
>Ubiquinone biosynthesis protein COQ7 homolog
MSCARALAACCLWRLRTGALQPLSAYGRRISVRFCSSGMTLDNINREAVDRIIRVDHAGE
YGANRIYAGQMAVLGRTSIGPVIQKMWDQEKDHLKKFNELMVAFRVRPTVLMPFWNVVGF
ALGAGTALLGKEGAMACTVAVEESIAHHYNNQIRTLMEKEPEKYEELLQVIKKFRDEELE
HHDIGLEHDAELAPAYVVLKSVIQAGCKVAIYLSERL
GenBank ID Protein AAI09579.1
UniProtKB/Swiss-Prot ID Q2TBW2
UniProtKB/Swiss-Prot Entry Name COQ7_BOVIN
PDB IDs Not Available
GenBank Gene ID BC109578
GeneCard ID COQ7
GenAtlas ID Not Available
HGNC ID Not Available
References
General References Not Available